Introduction: Congenital preaxial polydactyly is usually associated with varus deformity and syndactyly. To our knowledge, this is the first case report of a young child presented with unilateral preaxial polydactyly with two supernumerary rays extending up to accessory talus without varus deformity and syndactyly. Case description: We present here the case of a 7-year-old girl patient who was presented to us with untreated congenital preaxial polydactyly. A rare case of a young child presented with unilateral preaxial polydactyly with two supernumerary rays extending up to accessory talus without varus deformity and syndactyly. The patient had two extra-toes present on the medial side of her big toe which extended up to talus in her left foot. Surgical excision of complete ray was done. Conclusion: Surgical acceptance for preaxial polydactyly was quick as it created a barrier for normal walking and difficulty in wearing footwear. Postoperatively, the girl was followed up for 4 years and observed for any problem in varus deformity and foot mechanics.