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VOLUME 4 , ISSUE 2 ( July-December, 2022 ) > List of Articles

CASE REPORT

An Unusual Presentation of Buckling Collapse Type of Kyphoscoliosis in Neurofibromatosis: A Case Report

V Venkatasujith, Nitin Goyal, P C S Vishnu

Keywords : Buckling collapse type, Dystrophic type, Halo gravity traction, Neurofibromatosis, Thoracic myelopathy

Citation Information : Venkatasujith V, Goyal N, Vishnu PC. An Unusual Presentation of Buckling Collapse Type of Kyphoscoliosis in Neurofibromatosis: A Case Report. 2022; 4 (2):81-84.

DOI: 10.5005/jp-journals-10079-1083

License: CC BY-NC 4.0

Published Online: 31-05-2022

Copyright Statement:  Copyright © 2022; The Author(s).


Abstract

Spinal deformities such as kyphoscoliosis are the most common skeletal abnormalities in neurofibromatosis. Dystrophic type of spine deformities mostly progress over time, leading to significant morbidity and mortality to the patient, hence early surgical intervention is indicated. Here we are presenting 22 years, male with dystrophic type thoracic kyphoscoliosis, who presented unusually with worsening of thoracic myelopathy after halo gravity traction (HGT), to help in the subsequent surgical correction. In literature, for buckling collapse type of kyphosis, HGT is advised and there are very few reports of worsening of neurology with the application of HGT. Hence this case report will add to the literature of treatment of severe dystrophic spinal deformities in neurofibromatosis. Key messages: Dystrophic type of spinal deformities in neurofibromatosis progress without further intervention and worsening of neurology with halo gravity traction can be an unexpected consequence while treating these patients.


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